INTRODUCTION Pulmonary sequestration (PS) is a rare congenital malformation characterized by the formation of a separated, abnormal pulmonary tissue supplied by one or more aberrant systemic arteries. About 95% of the cases develop in the left inferior lobe. It can be classified as intra or extra-lobar depending on whether it is covered by pleura or not; being the intra-lobar (75%) the most common presentation. Irrigation is provided by vessels emerging from the aorta. The aberrant tissue does not participate in gas exchange; however