RESUMEN INTRODUCCION: El sindrome de Prune Belly (SPB), tambien conocido como el sindrome de Eagle Barrett, se caracteriza por una triada de anomalias que incluye grados variables de hipoplasia de la musculatura abdominal, anomalias del tracto urinario y criptorquidia bilateral. OBJETIVO: Se describe el caso de un paciente masculino con Sindrome de Prune Belly y se realiza una revision de la literatura sobre esta rara enfermedad. CONCLUSION: La caracteristica arrugada del abdomen similar a una ciruela pasa, le da el nombre al sindrome. Ademas, puede estar asociado a alteraciones cardiovasculares, respiratorias, ortopedicas y gastrointestinales. Palabras clave: Sindrome de abdomen en ciruela pasa, agenesia abdominal, anomalias del tracto urinario, criptorquidia. ABSTRACT INTRODUCTION: Prune-belly syndrome, also known as Eagle-Barrett syndrome is characterized by a triad of anomalies that include varying degrees of abdominal musculature hypoplasia, urinary tract anomalies, and bilateral cryptorchidism. OBJECTIVE: We describe the case of a male patient with Prune Belly Syndrome and we review the literature on this rare disease. CONCLUSIONS: The characteristic wrinkled, prune-like abdomen, gives the name to the syndrome. Can also be associated with cardiovascular, respiratory, orthopedic and gastrointestinal anomalies. Keywords: Syndrome Prune-Belly, abdominal muscle defciency, urinary tract abnormalities, cryptorchidism.