RESUMEN A continuacion, se presenta un paciente de 66 anos con alteracion en los movimientos oculares, asociado a mio-clonias, disartria y ataxia cerebelosa, secundario a un proceso parainfeccioso por citomegalovirus. Posteriormente, se revisa la fisiopatologia del sindrome de opsoclonus – mioclonus – ataxia, las etiologias del mismo y las opciones terapeuticas disponibles. Esta es una etiologia poco frecuente del sindrome, pues solo se encontro un caso reportado de opsoclonus mioclonus ataxia asociado a citomegalovirus.PALABRAS CLAVES. Ataxia, Citomegalovirus, Sindromes paraneoplasicos (DeCS). (Luis Zarco, Laura Gil, Sonia Patricia Millan, Felipe Pretelt. Sindrome de opsoclonus-mioclonus-ataxia (OMA) parainfeccioso secundario a infeccion por citomegalovirus. Acta Neurol Colomb 2011;27:?237-242). SUMMARY This paper reported a 66 years old patient, with eye movements alteration associated to myoclonus, cerebellar ataxia and dysarthria, secondary to a parainfectious process by cytomegalovirus. The physiopathology of the opsoclonus myoclonus ataxia syndrome, its etiologies and the available therapeutic options were checked, and turned out that it is not very common since only one previous published case associated to cytomegalovirus was found.KEY WORDS. Ataxia, Cytomegalovirus, Paraneoplastic Syndrome (MeSH).