Chronic inflammatory demyelinating polyneuropathy (CIDP) is a group of diseases with autoimmune pathology, which progresses o relapses within 8 weeks, usually with proximal and distal weakness. Other phenotypic variants include predominantly distal weakness, sensory predominant cases and multifocal with persistent conduction block. We present a patient with chronic, insidious distal paresthesia in the lower limbs, distal weakness and later progressive proximal weakness. After completing evaluation we conclude it corresponds to distal acquired demyelinating symmetric neuropathy (DADS), he received high-dose intravenous immunoglobulin, corticosteroids, and rituximab without significant improvement.