Background: Developmental venous anomalies are the most frequently encountered common form of vascular malformations, with a reported incidence of up to 2.6% in a series of 4,069 brain autopsies.Parenchymal veins are divided into superficial and deep draining veins.Cerebral cavernous malformations, also known as cavernomas or cavernous hemangiomas, are clusters of abnormal hyalinized capillaries with no intervening brain tissue.The medusa head sign is seen in a developmental venous anomaly, where multiple radially arranged tributaries drain into a larger vein.Methodology: A narrative review was carried out through various databases from January 2007 to February 2022; the search and selection of articles was carried out in journals indexed in English.The following keywords were used: developmental venous anomalies, cavernomas, medusa head