Introduction: Giant spinal thoracic dumbbell schwannoma is a benign tumor extremely rare in pediatric age, which may be associated with neurofibromatosis.Case description: A 14-year-old girl who presented paresthesia in the lower extremities and back pain of 6 months onset, with 2 weeks of neurological deficit progression, associated with clinical data of neurofibromatosis.Posterior total excision was performed in a single surgery with transpedicular instrumentation without complications.Conclusion: This is the second case of type IVb pediatric thoracic giant spinal schwannoma reported, and the largest extracted by single posterior route in a single surgical time without complications.