Introduction: Chordoma is a rare malignant bone tumor, originating from embryonic remnants of the notochord. It is more common in males, with the highest incidence between 40 and 60 years, with slow-growing behavior and rarely occurring metastases. They are located mainly in the cephalic extremities and lumbar-sacral. Treatment of its skull base and pharyngeal location is basically surgical, supplemented by radiotherapy.