Rhabdomyosarcoma (RMS) is a rare type of soft tissue malignant neoplasm that currently represents about 7% of cancers in children, it is found in a much smaller proportion in adults, which represents about 1% of cancers, the global incidence of RMS is 4.5/million people under 20 years of age. Alveolar rhabdomyosarcoma (ARMS) is a widely studied subtype in minors and very rarely in adults. The most common presentation in extremities is of the alveolar subtype, most frequently affecting the lower extremities. We present a narrative review based on a case report of a patient with alveolar rhabdomyosarcoma in a lower extremity