Se presenta el caso de una paciente adulta joven que consulta por fiebre, odinofagia y artralgias, acompañado de una erupción cutánea no pruriginosa, en el examen físico se encuentran adenomegalias y hepatomegalia y se solicitan laboratorios. Con ferritina elevada, leucocitosis y neutrofilia y anticuerpos negativos, mediante los criterios de Yamaguchi se realiza el diagnóstico y se da el manejo con corticoterapia, AINE y metrotexato, con una mejoría clínica posterior. We present the case of a young adult patient who consulted for odynophagia fever and arthralgias, accompanied by non-pruritic rash, on physical examination adenomegaly and hepatomegaly were found, laboratories were requested with elevated ferritin, leukocytosis and neutrophilia and negative antibodies, using Yamaguchi's criteria the diagnosis was made and management with corticotherapy, NSAIDs and methotrexate was given with subsequent clinical improvement.