Clear cell carcinoma represents only 3% of all adult malignant tumors worldwide and when we include single metastases to the neck, we find an incidence of only 0.09% -0.4%.Only isolated anecdotal cases have been reported in the literature.The objective of presenting this case is to describe the clinicopathological manifestations, as well as the diagnosis of metastases to a very rare site in clear cell renal carcinoma.We present the case of a 64-year-old female patient, of Guatemalan nationality, with a personal history of kidney stones, acute kidney injury 2 years ago, bilateral grade III venous insufficiency, chronic hypokalemias for 15 years and a family history of breast cancer (mother), cervical cancer (grandmother), pulmonary fibrosis (father).Currently, the treatment of clear cell renal cell carcinoma metastases is primarily palliative; however, there are new molecular targeted agents that have shown promising results as adjunctive therapy.