A clinical case of a 13 year old male patient with a malignant tumor in the mandibular body area with two years of evolution and associated pain is reported.It was initially diagnosed as low grade central mucoepidermoid carcinoma through Hematoxylin and Eosin (H-E) staining in multiple biopsies.Considering the clinical and radiographic characteristics of the lesion, it was necessary to confirm the diagnosis through Periodic acid-Schiff (PAS).The treatment involved hemimandibulectomy, neck emptying, and complementary radiotherapy.This article aims to present a rare occurrence of this type of intraosseous malignant tumor of glandular origin in a young patient.