Extragastrointestinal stromal tumors are rare mesenchymal neoplasms that can occur in the omentum and mesentery. Little is known about its prognosis and management, so it is important to consider this pathology in order to find an adequate multidisciplinary diagnosis and treatment. We present the clinical case of a patient of the third age of the city of Cuenca that presented a clinical picture of pain, abdominal distension, lack of elimination of gases and feces of 24h of evolution, the physical examination showed a distended abdomen, pain on palpation diffusely, increased hydro noise. He was surgically intervened where a tumor was found 80 cm from the mesoenterium-dependent ileocecal valve, approximately 7x6 cm that involved intestinal loops; Histopathology reported a CD 117 positive extra gastrointestinal stromal tumor; patient evolved favorably, walking began at 24 hours and liquid diet at 72 hours with good tolerance, medical discharge was decided on the fifth day after surgery. Start oncological treatment at 4 months after surgery with imatinib 400mg, currently a patient with favorable evolution without recurrence.