Numerous differential diagnoses in adults, including sebaceous cysts, metastatic tumors, hernias, and congenital anomalies, are still unknown in the umbilical region.The aim of this article is to review an infrequent pathology, which must be managed through appropriate treatment for patients with signs and symptoms, which are rarely clear and frequent, and are sometimes observed by doctors without being easily differentiated.Therefore, based on our experience, we want to report a case found in our institution, with an initial diagnosis of hernia and end of umbilical sebaceous cyst.We performed complete resection of the same, and its follow-up without any recurrence and with favorable aesthetic results.