A 65 year-old male patient with a one year-duration tumoral growth located in the upper lip was diagnosed on incisional biopsy as epithelial-myoepithelial carcinoma.After wide surgical excision the histopathological analysis revealed the lesion was composed predominantly (>90%) of adenoid cystic carcinoma.In new sections it was found a very small and isolated area of adenoid cystic carcinoma at the bottom of the incisional biopsy.As surgical margins were free of lesion, no adjuvant treatment was given.The occurrence of a transitory ischaemic attack at 36 months of follow-up led to a neurological and MRI evaluation, which disclosed a well-defined 3.5x3 cm lesion suggestive of metastasis, located on the right temporal area.The lesion was surgically removed and a histopathological diagnosis of neurocysticercosis was rendered.After 40 months of follow-up there is no evidence of recurrence.Conclusion: True hybrid tumors of salivary glands are rare and treatment in each case should be done according to the component with the higher aggressiveness.However, the occurrence of epithelial-myoepithelial carcinoma areas within an adenoid cystic carcinoma seems to be a frequent finding, and because both lesions share a common origin, some authors consider that this may not be a true hybrid neoplasm but a variant of the latter.