The extraskeletal mesenc hymal chondrosarcoma belongs to a group of infrequent malignant cartilaginous tumors, which are not obvious mainly in the bone.The most common site of such tumors is within the orbit, the central nervous system and the soft tissues of the lower limbs.The commitment is usually metastatic to the lung and lymph nodes, especially in adult patients, who have shown an increased mortality.The paper aims at presenting the case of male patient aged 14, who was admitted to our institution with a solid lesion located at the level of soft tissues in the posterior aspect of the right leg and whose histopathological study confirmed Extraskeletal mesenchymal chondrosarcoma (CME) and the literature review about the same.