Objective: To report the clinical presentation and oncologic outcomes of a series of patients who presented with an abdominal or pelvic mass and were diagnosed with a gastrointestinal stromal tumor (GIST).Methods: Data were obtained on all patients who presented with an abdominal or pelvic mass between September 2007 and June 2010 and who were ultimately diagnosed with a GIST.The patients' medical records were reviewed.A literature review was also conducted.Results: Six patients were identified who met the inclusion criteria.All six patients had a tumor in the intestinal tract arising from the small bowel.The mean tumor size was 12 cm (range, 6 to 22 cm).A complete resection was achieved in five of the six patients.There were no intraoperative complications; one patient had a postoperative complication.Two patients were treated with imatinib after surgery.The mean follow-up time was 32 months (range, 0.3 to 40 months).At the last follow-up, five of the six patients were without any evidence of disease.One patient died of an unrelated hepatic encephalopathy.The incidence in our institution is 3%.Conclusion: GISTs are uncommon; however, they should be considered in the differential diagnosis of patients presenting with an abdominal or pelvic mass.