Ectomesenchymal chondromyxoid tumor (ECMT) is a recently described benign tumor, with a striking predilection for the oral cavity. We present the case of a 26-year-old female complaining of a small polypoid lesion, in the right dorsal-anterior aspect of the tongue. The polypoid lesion was resected, and after histopathological analysis a diagnosis of ECMT was rendered. ECMT is a very rare tumor with only a few published cases, none of them in Colombia.